A rare case of bronchopulmonary sequestration associated with a hiatal hernia

ABSTRACT

Bronchopulmonary sequestrations (BPS) are rare congenital anomalies resulting in formation of non-functioning lung tissue separate from the rest of the tracheobronchial tree. A defining feature of BPS is their arterial supply from an anomalous systemic vessel. Depending on pleural envelopment and venous drainage, they are categorized into intra-lobar (ILS) BPS and extra-lobar (ELS) BPS. In rare cases; they may be associated with other congenital pulmonary airway malformations and hiatal hernias. Bronchopulmonary sequestrations are usually identified on CT angiography and may be missed on non-contrast imaging. Definitive treatment typically involves embolization followed by surgical resection. We present a rare case of intra-lobar pulmonary sequestration associated with a hiatal hernia.

Keywords: bronchopulmonary sequestration, intra-lobar sequestration, hiatal hernia, congenital lung lesions, respiratory system abnormalities.