A rare case of bronchopulmonary sequestration associated with a hiatal hernia

Abstract

Bronchopulmonary sequestrations (BPS) are rare congenital anomalies resulting in formation of non-functioning lung tissue separate from the rest of the tracheobronchial tree. A defining feature of BPS is their arterial supply from an anomalous systemic vessel. Depending on pleural envelopment and venous drainage, they are categorized into intra-lobar BPS and extra-lobar BPS. In rare cases, they may be associated with other congenital pulmonary airway malformations and hiatal hernias. BPS are usually identified on CT angiography and may be missed on non-contrast imaging. Definitive treatment typically involves embolization followed by surgical resection.  We present a rare case of intra-lobar pulmonary sequestration associated with a hiatal hernia.