Kokila Kakarala MDa, Tim Chen DO
Correspondence to Kokila Kakarala, MD.
Email: kokilak@gmail.com
SWRCCC 2015;3(11):15-18
doi: 10.12746/swrccc2015.0311.139
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A 28-year-old woman was admitted to the intensive care unit with severe respiratory distress secondary to uncontrolled asthma. In spite of standard acute asthma therapy, the patient’s mental status deteriorated, and she developed severe hypoxia requiring intubation. On day two of admission, the patient developed a fever of 38.7°C that persisted for four days without any known etiology after extensive laboratory work-up, chest x-rays, and an abdominal ultrasound. She is diagnosed with nosocomial fever of unknown origin. What is the appropriate work-up and management for patients with nosocomial fever of unknown origin, and what additional tests might help evaluate patients who are intubated?
Fever is often a self-limiting occurrence in which an etiology can be promptly determined. However, in some circumstances fever can persist for an extended period of time without an identifiable cause in spite of an extensive work-up. This clinical scenario is called fever of unknown origin (FUO).1,2 Four categories of FUO are defined in Table 1. All categories share a temperature threshold of >38.3°C with varying duration, patient location, and confounding diagnoses.
Table 1: Durack and Street classification of fever of unknown origin3 |
|
Category |
Distinguishing Factors |
Classic |
>3 weeks |
Nosocomial |
Patient hospitalized ≥24 hours without fever being present or incubating on admission |
Neutropenic |
Evaluation of at least 3 days with absolute neutrophil count ≤500 per mm3 |
HIV associated |
>4 weeks for outpatient and >3 days for inpatients with confirmed HIV infection |
In pediatric hematology/oncology patients, bacteremia and fever of unknown origin were identified as the most common nosocomial infections.4 In a study of adult hematology/oncology patients, 33 FUOs were documented in 116 patients hospitalized for a total of 4,002 days, with 66.7% of the FUOs occurring when the patients were neutropenic.5
FUOs have multiple causes, and the list of diagnoses has changed over time secondary to widespread use of antibiotics, increased knowledge of disease pathology, and advances in diagnostic testing. For example, early imaging utilization has decreased the proportion of FUO caused by intra-abdominal abscesses and tumors. Infection continues to be the predominant cause of FUO followed by neoplasms and noninfectious inflammatory diseases. FUO is often caused by atypical presentations of common diseases, with endocarditis, diverticulitis, vertebral osteomyelitis, and extrapulmonary tuberculosis being the most frequent. The prevalence of infection as a leading cause is even more significant in non-Western nations, where tuberculosis accounts for up to 50% of cases in some countries.2 In some cases nosocomial fever occurs in postoperative patients after the release of cytokines and interleukins from tissue injury and not infection.6 In a prospective cross sectional study conducted in pediatric and adult ICUs (n=63), 82% of patients with nosocomial FUO were found to have acute bacterial nosocomial sinusitis diagnosed by microbiological analysis of sinus fluid aspirates.7 Other common causes of nosocomial FUO include drug fever, health care associated infections, thrombosis, pulmonary embolism, and neoplasm.2
Evaluation of FUO
FUO is a diagnosis made after thorough history taking, physical examination, and obligatory investigations as listed in Table 2. No symptom should be regarded as irrelevant due to the likelihood of atypical manifestations of common diseases with FUO. Repeating the history taking by different members of the team and gathering information from family and friends of the patient can also be valuable.1,2
Table 2: Initial evaluation for FUO |
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Specific factors to address in history for suspected FUO1 |
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Sick contacts |
Prosthetic devices |
Living & working conditions |
Tuberculosis exposure |
Psychiatric illness |
Recreational activities |
Previous chronic infections |
Prescribed medications |
Dietary habits |
History of transfusions |
Over the counter medications |
Recreational drugs |
Diagnosis of malignancies |
Herbal remedies |
Sexual activity |
Immunosuppressive therapy |
Country of origin |
Animal exposure |
Indwelling foreign materials |
Vaccination status |
Travel history |
|
||
Specific factors to address in physical examination for suspected FUO1 |
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Fundi |
Thyroid gland |
Genital area |
Conjunctivae |
Lymphatic system |
Pulses |
Oropharynx |
Heart murmurs |
Skin |
Temporal artery |
Abdomen |
Joints |
|
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Obligatory laboratory and imaging investigations2 |
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Erythrocyte sedimentation rate |
Total protein |
Rheumatoid factor |
C-reactive protein |
Alkaline phosphatase |
Protein electrophoresis |
Platelet count |
Alanine aminotransferase |
Urinalysis |
Leukocyte count |
Aspartate aminotransferase |
Blood cultures (n=3) |
Leukocyte differential |
Lactate dehydrogenase |
Urine culture |
Electrolytes |
Creatine kinase |
Tuberculin skin test |
Creatinine |
Ferritin |
Chest x-ray |
Hemoglobin |
Antinuclear antibodies |
Abdominal ultrasonography |
In addition to imaging by chest x-ray and abdominal ultrasonography, computed tomography (CT) and magnetic resonance imaging (MRI) are often used. Since localizing signs or symptoms are often absent, clinicians have started to use positron emission tomography/computed tomography (PET/CT) to detect focal sites of inflammation.8 Sinusitis develops frequently in patients with orotracheal or nasotracheal intubation, limited mobilization, facial trauma, or prior sinus disease, and can be detected with sinus x-rays, ultrasound, or CT scans as part of the work-up for FUO.9
Our 28-year-old patient has nosocomial fever of unknown origin and is currently intubated. She underwent the obligatory laboratory and imaging studies done for an FUO work-up, and later had sinus x-rays due to her intubation status. Other considerations included drug fever and venous thromboembolic disease. Additionally, reevaluating the patient’s history and physical examination and speaking with family and friends of the patient brought attention to a previous history of sinus disease. With the additional studies our patient was found to have acute bacterial nosocomial rhinosinusitis and was started on the appropriate antibiotic treatment. Patients with FUO usually have good outcomes even without a diagnosis, and if there is no indication for a particular etiology, subsequent approaches include a “wait and see” strategy, whole body inflammation tracer scintigraphy, a staged approach, or therapeutic trials.10
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Received: 04/25/2015
Accepted: 05/10/2015
Reviewers: Richard Winn MD
Published electronically: 07/15/2015
Conflict of Interest Disclosures: none