Large atrial septal defect misdiagnosed as arrhythmogenic right ventricular cardiomyopathy

Lisa Moore DO, Cihan Cevik MD

ABSTRACT

We report a case of a large ostium secundum atrial septal defect that was initially diagnosed as an arrhythmogenic right ventricular cardiomyopathy. We discuss the initial workup, diagnosis, and treatment of this patient’s atrial septal defect and explore how the pathophysiology of arrhythmogenic right ventricular cardiomyopathy may mimic congenital heart disease when there is a large left-to-right shunt.

Keywords: atrial septal defect, arrhythmogenic right ventricular cardiomyopathy, arrhythmogenic right ventricular dysplasia, congenital heart disease, left to right shunt

Article citation: The Southwest Respiratory and Critical Care Chronicles 2019;7(30):58–62
From: Rocky Vista University College of Osteopathic Medicine, UC Health Heart Center Memorial Hospital Central, Colorado Springs, CO.
Submitted: 5/9/2019
Accepted: 7/1/2019
Reviewers: Scott Shurmur MD; Aliakbar Arvandi MD
Conflicts of interest: none
This work is licensed under a Creative Commons Attribution-ShareAlike 4.0 International License.