Pulmonary artery aneurysm secondary to congenital pulmonic valve stenosis
Abstract
Pulmonary artery (PA) aneurysms are uncommon and often diagnosed post-mortem. They are characterized by a PA/aorta diameter ratio greater than 2 on transthoracic echocardiography or a pulmonary artery diameter greater than 4 or 5 cm on computed tomography. The most common conditions associated with pulmonary artery aneurysm are congenital heart defects with left-to-right shunts and pulmonic valve abnormalities. There are also numerous causes of acquired pulmonary artery aneurysms, including infection, vasculitis, pulmonary arterial hypertension, trauma, neoplasm and pulmonary embolism. Symptoms of PA aneurysm are usually non-specific, and physical examination findings are variable depending on the underlying cause. Work-up includes various imaging modalities, transthoracic echocardiography, and right heart catheterization. The gold standard treatment is surgery, but in select patients, conservative management with close monitoring can be pursued.
Keywords: Pulmonic valve stenosis, pulmonary artery aneurysm, hilar mass
Downloads
References
Kreibich M, et al. Aneurysms of the pulmonary artery.
Circulation
;131:310–316.
Lopez-Candales A, et al. Pulmonary artery aneurysm: review
and case report. Clinical Cardiology 1995;18:12:738–740.
Tami L, McElderry M. Pulmonary artery aneurysm due to
severe congenital pulmonic stenosis. Angiology May 1994;
:5;383–389.
Shankarappa R K, et al. Giant pulmonary artery aneurysm
secondary to primary pulmonary hypertension. Texas Heart
Institute Journal 2010;37:2;244–245.
Shafiq A, Bokhari A, Nahin I, et al. Extreme dilation of
pulmonary artery: a literature review. BMJ Case Rep 2014
casereports.bmj.com/content/2014/bcr-2013-202223.full.
Shindo T, et al. Aneurysmal dilatation of the pulmonary
trunk with mild pulmonic stenosis. Internal Medicine1995;
:199–202.
