Large atrial septal defect misdiagnosed as arrhythmogenic right ventricular cardiomyopathy
We report on a case of a large ostium secundum atrial septal defect (ASD) that was initially diagnosed as arrhythmogenic right ventricular cardiomyopathy (ARVC). We discuss the initial work up, diagnosis, and treatment of this patient’s ASD and explore how the pathophysiology of ARVC may mimic congenital heart disease where there is a large left-to-right shunt.
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